SCN5A Variant S943N

Summary of observed carriers, functional annotations, and structural context for SCN5A S943N. Data combine curated literature, international cohorts, and gnomAD observations.

Estimated LQT3 penetrance

14%

0/11 effective observations

Estimated BrS1 penetrance

5%

0/11 effective observations

Total carriers

1

0 BrS1 · 0 LQT3 · 1 unaffected

S943N is present in 1 alleles in gnomAD. This residue resides in a Non_Hotspot region for Brugada syndrome and a Mild_Hotspot region for LQT3.

Variant features alone are equivalent to phenotyping 0 individuals for Brugada syndrome and 0 individuals for LQT3.

In silico predictors

Variant-level computational predictors.
PROVEAN PolyPhen-2 BLAST-PSSM REVEL Penetrance Density BrS (%) Penetrance Density LQT3 (%)
-2.93 0.985 2.51 0.85 1 17

PROVEAN scores below -2 suggest deleterious impact. REVEL scores above 0.5–0.75 are often interpreted as likely pathogenic. PolyPhen-2 scores above 0.85 are typically pathogenic. Penetrance density summarises neighbouring residue risk (Kroncke et al. 2019).

Reported carrier data

Observed carriers by publication or cohort.
Source Year Carriers Unaffected LQT3 BrS1 Other Other Disease
Literature, cohort, and gnomAD 1 1 0 0
Variant features alone 15 15 0 0

Totals may differ from individual publications due to duplicate patients removed during curation.

Nearby variants

Neighbouring residues within 15 Ångström provide structural context. Variants listed in the right-most column have been observed clinically or in gnomAD.

Previously observed variants near S943N.
Neighbour residue Distance (Å) Observed variants
939 7 L939F,
937 11
1773 14
943 0 S943N,
1472 11 p.N1472del, N1472S,
1487 12 M1487L, M1487L, M1487K,
1333 13
417 11
934 15
1471 7
935 13 L935P,
1470 10
1464 12 c.4389_4396delCCTCTTTA, L1464P,
1466 13 c.4396_4397insG,
1478 14 K1478E,
944 4
830 13
833 15 G833R, G833R,
1769 15
940 6 S940N,
1473 14 F1473S, F1473C,
1468 9 V1468F, V1468A,
831 9
420 13
938 9
1474 11
942 6
834 12 N834D,
1772 15 L1772V
827 12
1460 15 F1460L, F1460L, F1460L,
416 13 Y416C,
413 14 A413T, A413E,
941 6 S941N, S941F,
1337 15
936 11
1467 9
1484 15
421 14
1475 12 p.Q1475NfsX6, Q1475L,
1469 13 I1469V,
832 13
835 13 S835A, S835L,
828 13 L828V,
1489 14 E1489D, E1489D,